STOMATOLOGIC MANAGEMENT OF A CHILD PATIENT WITH DUCHENNE MUSCULAR DYSTROPHY. CASE REPORT
DOI:
https://doi.org/10.31984/oactiva.v1i2.138Keywords:
Duchenne muscular dystrophy, pediatric dentistry, dystrophinAbstract
Duchenne muscular dystrophy (DMD) is an X linked condition that affects approximately 1 in 3300 live male births. It is caused by the absence or disruption of the protein dystrophin. The purpose of this case was to review the current literature about the important aspects of the DMD in children. CASE PRESENTATION: An 8 year old male patient arrives to the pediatric dentistry clinic with a walking disability and ectomorphic constitution, diagnosed with DMD. At the intraoral examination was found: neutrocclusion, edge-to-edge incisor relationship, diastemas, lower anterior crowding, localized gingivitis, active caries lesions and relative macroglossia. The stomatologic management was conducted in four phases: Preventive phase, Restorative phase, Surgical phase and Maintenance phase. A successful clinical approach was achieved, needing a highly specialized multidisciplinary work to provide satisfactory results that increases the quality of life of this patient.
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